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Steward-Treves syndrome in a male patient

Sonya Marina, Paula Lozanova, Valentina Broshtilova, Kosara Drenovska, Dimitrina Serafimova, Irina Yungareva, Dimitrina Guleva

Abstract

Lymphangiosarcoma is an uncommon vascular tumor that usually develops in chronic lymphedema. The etiology of lymphangiosarcoma remains unknown. It develops mainly after mastectomy, in association with chronic lymphedema (Stewart-Treves syndrome), or after radiotherapy. The early diagnosis of this aggressive tumor is important, as it has a high risk of local recurrence and metastasis. Stewart-Treves syndrome occurs in 0.5% of patients who survive mastectomy for more than 5 years. The mean age at appearance of the angiosarcoma is 62 years, and the mean interval between mastectomy and the appearance of the tumour is 10.5 years. Only two cases have been reported in men following mastectomy. We present a 70-year old male patient with lymphangiosarcoma which developed three and a half years after the diagnosis of breast carcinoma. The patient underwent mastectomy of the right mammary gland with ipsilateral axillary lymph node dissection and had postoperative chemo- and radiotherapy.


Keywords

lymphangiosarcoma; Steward-Treves syndrome; chronic lymphoedema; mastectomy

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DOI: http://dx.doi.org/10.14748/ssm.v46i1.650

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About The Authors

Sonya Marina
University Hospital Alexandrovska of Sofia
Bulgaria

Department of Dermatology and Venereology

Paula Lozanova
University Hospital Alexandrovska of Sofia
Bulgaria

Department of Dermatology and Venereology

Valentina Broshtilova
University Hospital Alexandrovska of Sofia
Bulgaria

Department of Dermatology and Venereology

Kosara Drenovska
University Hospital Alexandrovska of Sofia
Bulgaria

Department of Dermatology and Venereology

Dimitrina Serafimova
University Hospital Alexandrovska of Sofia
Bulgaria

Department of Dermatology and Venereology

Irina Yungareva
University Hospital Alexandrovska of Sofia
Bulgaria

Department of Dermatology and Venereology

Dimitrina Guleva
University Hospital Alexandrovska of Sofia
Bulgaria

Department of Dermatology and Venereology

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