Coats disease is a rare, in about 90% of cases unilateral idiopathic eye pathology. It is characterized by telangiectatic and aneurysmally altered retinal blood vessels and progressive intra- and subretinal exudation, which can lead to exudative retinal detachment. Most often the symptoms manifest in the advanced stages. Purpose: To report a case with Coats disease. 10 year old boy, admitted to the Eye Clinic of the University Alexandrovska Hospital – Sofia, with leucocoria and strabismus of the right eye. Method: Full ophthalmic and orthoptic examination, OCT. Results: 3B stage of Coats disease of the right eye was established. The chance for improvement after surgery was evaluated as very little, so our patient remained under observation with protective glasses and prevention of complications. Conclusion: It is of great importance to early diagnose the disease, so to have more treatment options.
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