Straatsma`s syndrome. Ipsilateral myelinated retinal nerve fibres, axial myopia, amblyopia syndrome

N. Veleva; A. Oscar; P. Kemilev; V. Chernodrinska

doi:10.14748/bro.v0i1.4523

Straatsma`s syndrome. Ipsilateral myelinated retinal nerve fibres, axial myopia, amblyopia syndrome

N. Veleva, A. Oscar, P. Kemilev, V. Chernodrinska

Abstract

Myelinated retinal nerve fibers (MRNF) or so called fibrae medullaris retinae are rare congenital anomaly. In most cases it is isolated ocular pathology, usually asymptomatic and diagnosed accidentally. They may present in a syndrome characterised by ipsilateral myelinated retinal nerve fibres, axial myopia and amblyopia - triad of Straatsma. We report three cases of this rare congenital condition.

Keywords

myelinated retinal nerve fibres; amblyopia; axial myopia; Straatsma`s syndrome

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DOI: http://dx.doi.org/10.14748/bro.v0i1.4523