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Scripta Scientifica Medica

Systematized epidermolytic epidermal nevus (ichthyosis hystrix)

Sonya Márina, Kristina Semkova, Jana Kazandjieva, Dimitrina Guleva

Abstract

Ichthyosis hystrix is a term used to describe an autosomal dominant rare form of an ichthyosiform dermatosis which is characterized by hyperkeratotic spiny scales. We present a healthy 22-year-old man with lesions which clinically and histopathologically corresponded to the rare inherited disorder ichthyosis hystrix.

Keywords

systematized epidermal nevus, congenital hamartomas, epidermolytic hyperkeratosis

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References

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DOI: http://dx.doi.org/10.14748/ssm.v47i3.1292
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About The Authors

Sonya Márina
Medical University - Sofia, Bulgaria Dep. of Dermatology and Venereology
Bulgaria

Kristina Semkova
Medical University - Sofia, Bulgaria Dep. of Dermatology and Venereology
Bulgaria

Jana Kazandjieva
Medical University - Sofia, Bulgaria Dep. of Dermatology and Venereology
Bulgaria

Dimitrina Guleva
Medical University - Sofia, Bulgaria Dep. of Dermatology and Venereology
Bulgaria

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